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Pemphigus vulgaris is a rare autoimmune disease that is characterised by painful blisters and erosions on the skin and mucous membranes, most commonly inside the mouth. Pemphigus vulgaris accounts for 70% of all pemphigus cases worldwide although it is extremely rare in New Zealand (about one case per million of the population).
Pemphigus foliaceus is an autoimmune disorder, which basically means that an individual's immune systems starts reacting against his or her tissue. The building block cells of the epidermis are called keratinocytes. These cells are cemented together at special sticky spots called desmosomes.
2021年11月15日 · IgA pemphigus (or immunoglobulin A pemphigus) is an autoimmune blistering disorder. It is also called intercellular IgA dermatosis among other names. IgA pemphigus has two major subtypes: Subcorneal pustular dermatosis (SPD) type. Deposition of intracellular IgA against the glycoprotein desmocollin-1 seen predominantly in the upper epidermis.
Pemphigus — extra information Categories: Autoimmune/autoinflammatory ICD-10: L10 ICD-11: EB 40.Z SNOMED ...
Bullous pemphigoid causes severe itch and (usually) large, tense bullae (fluid-filled blisters), which rupture forming crusted erosions. Other variable features include: Bullous pemphigoid typically involves the flexor aspects of the limbs. It may be localised to one area, or widespread on the trunk and proximal limbs.
Pemphigoid nodularis is a rare nodular variant of bullous pemphigoid. There is limited literature on pemphigoid nodularis to date, with only case reports describing the condition. It was first described by Provost et al in 1979 and Yung et al in 1981. Credit: Das D, Bandyopadhyay D. Juvenile pemphigoid nodularis: Report of a rare case.
Pemphigus vulgaris is a rare autoimmune disease that is characterised by painful blisters and erosions on the skin and mucous membranes, most commonly inside the mouth. View pictures of pemphigus vulgaris in the gallery below.
What is paraneoplastic pemphigus? Paraneoplastic pemphigus (PNP) is a rare, autoimmune, mucocutaneous, blistering disease that is almost always associated with a confirmed or occult neoplasm. Paraneoplastic autoimmune multiorgan syndrome (PAMS) is another proposed name for PNP due to potential autoimmune reactions also appearing in internal ...
Eye involvement affects people with autoimmune blistering skin diseases to a varying degree. It is seen most commonly in: Paraneoplastic pemphigus. While ocular involvement in bullous pemphigoid, pemphigus foliaceus, and dermatitis herpetiformis has also been reported, it is much less common.
2017年8月2日 · Benign familial pemphigus is also known as Hailey–Hailey disease. It is a rare hereditary blistering skin disease first described by the Hailey brothers in 1939. Unrelated to pemphigus vulgaris, Hailey-Hailey disease is not an autoimmune condition and has a differing prognosis. Hailey-Hailey disease in axilla.
